HEMOFILIA ADQUIRIDA IDIOPÁTICA: UM RELATO DE CASO
DOI:
https://doi.org/10.63845/t2xfc239Keywords:
Hemofilia. Fator VIII. Autoanticorpos.Abstract
A hemofilia adquirida idiopática é uma condição médica extremamente rara, causada pelo desenvolvimento espontâneo de autoanticorpos contra o fator VIII (FVIII), com incidência estimada em 1,5/milhão de habitantes/ano. Embora esteja descrita a associação com outras doenças, seu fator precipitante é desconhecido. O quadro clínico se caracteriza por hemorragias graves, sem história pessoal ou familiar prévia de coagulopatias. Os autores relatam um caso clínico de hemofilia adquirida idiopática com evolução desfavorável.
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