NASAL WING NEUROFIBROMA SURGICAL TREATMENT

Authors

  • Mike Fernando Pizarro Herrera Serviço de Cirurgia Plástica e Queimados do HU-UFSC
  • Marlei Sangalli Serviço de Cirurgia Plástica e Queimados do HU-UFSC
  • Karina Meneguzze Serviço de Cirurgia Plástica e Queimados do HU-UFSC
  • Pablo Marcelo Vimos Gomez Serviço de Cirurgia Plástica e Queimados do HU-UFSC
  • José Paulo Tapie Barbosa Serviço de Cirurgia Plástica e Queimados do HU-UFSC
  • Zulmar Accioli de Vasconcellos Serviço de Cirurgia Plástica e Queimados do HU-UFSC

Keywords:

Neurofibromatosis, Excision, Surgical treatment

Abstract

Introduction: Neurofibromatosis is a neurocutaneous syndrome caused by several genetic mutations that commonly affect the nervous system and skin. It is characterized by overlapping clinical manifestations, causing benign or malignant tumors. Objective: To approach through the surgical excision a neurofibroma in the nasal ala and chin of a patient with neurofibromatosis type 1 to correct a deformity, a condition that has occurred since childhood. Methods: After the plan was traced, a procedure to remove the lesions was performed using conventional drying, with enucleation of the neurofibroma and reconstruction of the nasal ala. Results: Surgical treatment was successful and showed good evolution. The patient reported being satisfied and improving his quality of life due to the results obtained. Conclusion: After approaching, the patient reported being satisfied, with a significant improvement in quality of life associated with facial deformities that affected his self-esteem. The surgical approach with conventional resecting of the lesions proved effective, bringing positive results.

Author Biographies

  • Mike Fernando Pizarro Herrera, Serviço de Cirurgia Plástica e Queimados do HU-UFSC

    Residente do Serviço de Cirurgia Plástica HU/UFSC.

  • Marlei Sangalli, Serviço de Cirurgia Plástica e Queimados do HU-UFSC

    Residente do Serviço de Cirurgia Plástica HU/UFSC.

  • Karina Meneguzze, Serviço de Cirurgia Plástica e Queimados do HU-UFSC

    Residente do Serviço de Cirurgia Plástica HU/UFSC.

  • Pablo Marcelo Vimos Gomez, Serviço de Cirurgia Plástica e Queimados do HU-UFSC

    Residente do Serviço de Cirurgia Plástica HU/UFSC

  • José Paulo Tapie Barbosa, Serviço de Cirurgia Plástica e Queimados do HU-UFSC

    Preceptor do Serviço de Cirurgia Plástica HU/UFSC/EBSERH

  • Zulmar Accioli de Vasconcellos, Serviço de Cirurgia Plástica e Queimados do HU-UFSC

    Membro Titular da Sociedade Brasileira de Cirurgia Plástica. Regente do Serviço de Cirurgia Plástica HU/UFSC.

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Published

2022-04-28

How to Cite

NASAL WING NEUROFIBROMA SURGICAL TREATMENT. (2022). Arquivos Catarinenses De Medicina, 51(1), 334-340. https://revista.acm.org.br/arquivos/article/view/1218

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